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Results 1 to 25 of 197

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SECRETION OF BETA -HEXOSAMINIDASE BY CULTURED HUMAN SKIN FIBROBLASTS. KINETICS, EFFECT OF TEMPERATURE, CELL DENSITY, SERUM CONCENTRATION AND PH.VON FIGURA K.1978; EXPER. CELL RES.; U.S.A.; DA. 1978; VOL. 111; NO 1; PP. 15-21; BIBL. 16 REF.Article

HUMAN ALPHA -N-ACETYLGLUCOSAMINIDASE. I. PURIFICATION AND PROPERTIES.VON FIGURA K.1977; EUROP. J. BIOCHEM.; GERM.; DA. 1977; VOL. 80; NO 2; PP. 525-533; BIBL. 29 REF.Article

HUMAN ALPHA -N-ACETYLGLUCOSAMINIDASE. II. ACTIVITY TOWARDS NATURAL SUBSTRATES AND MULTIPLE RECOGNITION FORMS.VON FIGURA K.1977; EUROP. J. BIOCHEM.; GERM.; DA. 1977; VOL. 80; NO 2; PP. 535-542; BIBL. 30 REF.Article

BIOCHEMIE UND FUNKTION DER GLYKOSAMINOGLYKANE DER HAUT. = BIOCHIMIE ET FONCTION DES GLYCOSAMINOGLYCANES DE LA PEAUVON FIGURA K.1976; HAUTARZT; DTSCH.; DA. 1976; VOL. 27; NO 5; PP. 206-213; ABS. ANGL.; BIBL. 46 REF.Article

EFFECT OF TUNICAMYCIN ON THE METABOLISM OF LOW-DENSITY LIPOPROTEINS BY CONTROL AND LOW-DENSITY-LIPOPROTEIN-RECEPTOR-DEFICIENT HUMAN SKIN FIBROBLASTSFILIPOVIC I; VON FIGURA K.1980; BIOCHEM. J.; GBR; DA. 1980; VOL. 186; NO 1; PP. 373-375; BIBL. 20 REF.Article

OLIGOSACCHARIDES IN LYSOSOMAL ENZYMES. DISTRIBUTION OF HIGH-MANNOSE AND COMPLEX OLIGOSACCHARIDES IN CATHEPSIN D AND BETA -HEXOSAMINIDASEHASILIK A; VON FIGURA K.1981; EUR. J. BIOCHEM.; ISSN 0014-2956; DEU; DA. 1981; VOL. 121; NO 1; PP. 125-129; BIBL. 23 REF.Article

CHARACTERIZATION OF DERMATAN SULFATE IN MUCOPOLYSACCHARIDOSIS. VI. EVIDENCE FOR THE ABSENCE OF HYALURONIDASE-LIKE ENZYMES IN HUMAN SKIN FIBROBLASTSKLEIN U; VON FIGURA K.1980; BIOCHIM. BIOPHYS. ACTA; NLD; DA. 1980; VOL. 630; NO 1; PP. 10-14; BIBL. 17 REF.Article

PARTIAL PURIFICATION AND CHARACTERIZATION OF A HEPARAN SULFATE SPECIFIC ENDOGLUCURONIDASE.KLEIN U; VON FIGURA K.1976; BIOCHEM. BIOPHYS. RES. COMMUNIC.; U.S.A.; DA. 1976; VOL. 73; NO 3; PP. 569-576; BIBL. 14 REF.Article

SUBSTRATE SPECIFICITY OF A HEPARAN SULFATE-DEGRADING ENDOGLUCURONIDASE FROM HUMAN PLACENTAKLEIN U; VON FIGURA K.1979; Z. (HOPPE-SEYLER'S) PHYSIOL. CHEM.; DEU; DA. 1979; VOL. 360; NO 10; PP. 1465-1471; ABS. GER; BIBL. 17 REF.Article

DEMONSTRATION D-GLUCURONIC ACID AS REDUCING TERMINAL OF INTRACELLULAR HEPARAN SULFATES.KLEIN U; VON FIGURA K.1976; F.E.B.S. LETTERS; NETHERL.; DA. 1976; VOL. 71; NO 2; PP. 266-268; BIBL. 10 REF.Article

INHIBITION OF PINOCYTOSIS BY CYTOCHALASINB. DECREASE IN INTRACELLULAR LYSOSOMAL-ENZYME ACTIVITIES AND INCREASED STORAGE OF GLYCOSAMINOGLYCANSVON FIGURA K; KRESSE H.1974; EUROP. J. BIOCHEM.; GERM.; DA. 1974; VOL. 48; PP. 357-363; BIBL. 30REF.Article

THE SANFILIPPO B CORRECTIVE FACTOR: A N-ACETYL-ALPHA -D-GLUCOSAMINIDASEVON FIGURA K; KRESSE H.1972; BIOCHEM. BIOPHYS. RES. COMMUNIC.; U.S.A.; DA. 1972; VOL. 48; NO 2; PP. 262-269; BIBL. 12 REF.Serial Issue

HUMAN PLACENTA ALPHA -N-ACETYLGLUCOSAMINIDASE: PURIFICATION, CHARACTERIZATION AND DEMONSTRATION OF MULTIPLE RECOGNITION FORMSROEHRBORN W; VON FIGURA K.1978; Z. (HOPPE-SEYLER'S) PHYSIOL. CHEM.; DEU; DA. 1978; VOL. 359; NO 10; PP. 1353-1362; ABS. GER; BIBL. 27 REF.Article

AN ALTERNATIVE HYPOTHESIS OF CELLULAR TRANSPORT OF LYSOSOMAL ENZYMES IN FIBROBLASTS: EFFECT OF INHIBITORS OF LYSOSOMAL ENZYME ENDOCYTOSIS ON INTRA- AND EXTRA-CELLULAR LYSOSOMAL ENZYME ACTIVITIESVON FIGURA K; WEBER E.1978; BIOCHEM. J.; GBR; DA. 1978; VOL. 176; NO 3; PP. 943-950; BIBL. 23 REF.Article

ENDOCYTOSIS OF BETA -N-ACETYLGLUCOSAMINIDASE FROM SECTIONS OF MUCOLIPIDOSIS. II- AND III-FIBROBLASTS BY NON-PARENCHYMAL RAT LIVER CELLSULLRICH K; VON FIGURA K.1979; BIOCHEM. J.; GBR; DA. 1979; VOL. 182; NO 1; PP. 245-247; BIBL. 23 REF.Article

ISOLATION AND CHARACTERIZATION OF PHOSPHORYLATED OLIGOSACCHARIDES FROM ALPHA -N-ACETYLGLUCOSAMINIDASE THAT ARE RECOGNIZED BY CELL-SURFACE RECEPTORSVON FIGURA K; KLEIN U.1979; EUROP. J. BIOCHEM.; DEU; DA. 1979; VOL. 94; NO 2; PP. 347-354; BIBL. 33 REF.Article

ADHESION OF HUMAN SKIN FIBROBLASTS. EFFECT OF TETRAVALENT, DIVALENT AND MONOVALENT CONCANAVALIN APRINZ R; VON FIGURA K.1978; EXPER. CELL RES.; USA; DA. 1978; VOL. 112; NO 2; PP. 275-279; BIBL. 17 REF.Article

SANFILIPPO DISEASE TYPE B: PRESENCE OF MATERIAL CROSS REACTING WITH ANTIBODIES AGAINST ALPHA -N-ACETYLGLUCOSAMINIDASEVON FIGURA K; KRESSE H.1975; EUROP. J. BIOCHEM.; GERM.; DA. 1975; VOL. 61; PP. 581-588; BIBL. 22 REF.Article

PROCESSING OF THE PHOSPHORYLATED RECOGNITION MARKER IN LYSOSOMAL ENZYMES: CHARACTERIZATION AND PARTIAL PURIFICATION OF A MICROSOMAL ALPHA -N-ACETYLGLUCOSAMINYL PHOSPHODIESTERASEABDUL WAHEED; HASILIK A; VON FIGURA K et al.1981; J. BIOL. CHEM.; ISSN 0021-9258; USA; DA. 1981; VOL. 256; NO 11; PP. 5717-5721; BIBL. 30 REF.Article

EFFECT OF LECTINS ON ENDOCYTOSIS AND SECRETION OF LYSOSOMAL ENZYMES BY CULTURED FIBROBLASTSBEECK H; ULLRICH K; VON FIGURA K et al.1979; BIOCHIM. BIOPHYS. ACTA; NLD; DA. 1979; VOL. 583; NO 2; PP. 179-188; BIBL. 24 REF.Article

SPECIFIC BINDING OF SULFATED PROTEOGLYCANS TO CONCANAVALIN A. SEPHAROSE 4BSCHWERMANN J; PRINZ R; VON FIGURA K et al.1978; BIOCHEM. BIOPHYS. RES. COMMUNIC.; USA; DA. 1978; VOL. 83; NO 1; PP. 241-246; BIBL. 14 REF.Article

ACTION OF CHONDROITINASES ABC AND AC ON CHONDROITIN 4-SULFATE-OLIGOSACCHARIDES WITH TERMINAL N-ACETYLGALACTOSAMINITOL RESIDUES.KLINGBEIL U; KLEIN U; VON FIGURA K et al.1978; Z. (HOPPE-SEYLER'S) PHYSIOL. CHEM.; DEU; DA. 1978; VOL. 359; NO 6; PP. 765-767; ABS. GER; BIBL. 9 REF.Article

CHARACTERIZATION OF GLYCOSAMINOGLYCANS STORED IN MUCOPOLYSACCHARIDOSIS III A: EVIDENCE FOR A GENERALLY OCCURRING DEGRADATION OF HEPARAN SULFATE BY ENDOGLYCOSIDASES.KINDLER A; KLEIN U; VON FIGURA K et al.1977; Z. (HOPPE-SEYLER'S) PHYSIOL. CHEM.; DTSCH.; DA. 1977; VOL. 358; NO 11; PP. 1431-1438; ABS. ALLEM.; BIBL. 26 REF.Article

STORAGE OF MANNOSE-CONTAINING MATERIAL IN CULTURED HUMAN MANNOSIDOSIS CELLS AND METABOLIC CORRECTION BY PIG KIDNEY ALPHA -MANNOSIDASE.MERSMANN G; VON FIGURA K; BUDDECKE E et al.1976; Z. (HOPPE-SEYLER'S) PHYSIOL. CHEM.; DTSCH.; DA. 1976; VOL. 357; NO 5; PP. 641-648; ABS. ALLEM.; BIBL. 37 REF.Article

STIMULATION OF HEPARAN SULPHATE SYNTHESIS IN CULTURED RAT HEPATOCYTES BY (+)-CATECHINSINN W; SUDHAKARAN PR; VON FIGURA K et al.1981; BIOCHEM. J. (LOND.); ISSN 0006-2936; GBR; DA. 1981; VOL. 200; NO 1; PP. 51-57; BIBL. 23 REF.Article

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